
Recently a number of television shows, documentaries and circulating picture sets have generated great interest in the genetic phenomena of primordial dwarfism. These tiny people, these seemingly fragile, delicate and near ethereal human beings conjure images of gossamer fairies and quaint folk stories. Such enchanting imagery is likely the root of this new interest in the condition.
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The true tale of Edward Mordake (Mordrake) has been lost to history. His unusual case occurred early in medical history and is referenced only in tales handed down. Indeed, the tale of his life has become so muddled through the passage of time that no solid date of birth or death is evident to modern researchers. The story always begins the same way. Edward is said be have been heir to one of the noblest families in
In some versions of the story, the second face of Edward is a beautiful girl. This is an impossibility as all parasitic twins are of the same sex. Often it was said that it possessed its own intelligence and was quite malignant in its intentions. It has been said that the eyes would follow spectators and its lips would ‘gibber’ relentlessly and silently. According to legend it would smile and sneer as Edward wept over his condition. While no voice was ever audible, Edward swore that often he would be kept awake by the hateful whispers of his ‘evil twin’.
The story has always concluded with young Edward committing suicide at the age of twenty-three. The method of his death also differs, sometimes poison does him in and in other versions a bullet ‘between the eyes of his devil-twin’ puts him out of his misery. In both versions Edward leaves behind a letter requesting that the 'demon face' be destroyed before his burial, 'lest it continues its dreadful whisperings in my grave.'
Is the story of Edward true? The 1896 text Anomolies and Curiosities of Medicine mentions a version of the story and Edward has been featured in many texts, plays and even music as the Tom Waits song ‘Poor Edward’ is based on the story. However, the tale was considered false for quite some time. It was simply too fantastic to believe and, obviously, many parts of the story simply do not make medical sense – years of retelling warped what was likely a very real occurrence.
Chang Tzu Ping was discovered in
It does not require a great leap of faith to conclude that the tale of Edward is based on some nugget of fact, perhaps he had something similar Chang’s condition – mutated by storytellers over time. Consider that the case of Chang Tzu Ping is relatively unknown despite only occurring a few decades ago or the strange tale of The Boy of Bengal. These are indeed very rare cases and the human mind has a tendency to classify the unusual as impossible – it often helps us sleep well at night.
Listen to the Tom Wait song inspired by Edward Mordrake.
Skin tone is often a hot social topic. The conversations surrounding the perceived rights of ‘visible minorities’ has long been a heated one. However, what if your skin color placed you in a tiny minority? A tiny and very blue visible minority.The most famous of the blue people were the Fugates family. The blue Fugates weren't a race but rather an excessively tight-knit family living in the Appalachian Mountains. The patriarch of the clan was Martin Fugate, who settled along the banks of Troublesome Creek near Hazard, Kentucky, sometime after 1800. His wife, Mary, is thought to have been a carrier for a rare disease known as hereditary methemoglobinemia. Methemoglobinemia, in short, is a disease that causes blood to carry less oxygen which makes the skin of a Caucasian person display a bluish appearance due to the lack of oxygen. It is usually a recessive condition however the Fugate family intermarried with another clan, the Smith’s, and someone in that family carried the same recessive gene. Because of the small size of the community the family continued to inbreed and the family continued to display the unusual color trait well into the 1960’s.
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Images of persons afflicted with elephantiasis often crop up online and for decades the condition had been wrongfully fingered as the cause of the deformities distressing Joseph ‘The Elephant Man’ Merrick. For the record, Merrick likely suffered from Proteus syndrome; however the public mind continues to associate his bulbous and sagging appearance with the symptoms presented by elephantiasis.
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Over one thousand years before Homer, there exists a written account by Egyptian Pepy II of the 6th dynasty in which he urges one of his generals to look after a pygmy discovered on an expedition to the south. Furthermore, Amenemope at the end of the 2nd millennium B.C.E. set down laws to protect those born different from the norm:Seneb was a 4th or early 5th Dynasty dwarf and was chief of the royal wardrobe and priest of the funerary cults of Khufu. A statue still exists of him and it depicts him with his family - including his wife who was of normal stature. Also, the Egyptian gods Bes and Ptah were often depicted as dwarves. To say that dwarves were accepted and often revered members of ancient Egyptian society would be an understatement.
Dwarfism was unusually common in ancient
Dwarves are not to be confused with pigmies though. Pygmies are and entire race of persons of small stature first extensively written of by Homer in the Iliad. The Geranomachia, or pygmy war, was a popular topic for ancient writers and during the early modern age naturalist were clamoring to ‘rediscover’ the pygmies. In the late 1699, Edward Tyson wrote a lengthy paper on a pygmy he dissected attempting to prove that the creature was not human and thus modern man was superior. He proved to be correct in his first assumption as, looking back on the document; the pygmy was actually a chimpanzee.
The first pygmy to be rediscovered was named Akadimoo and belonged to the ‘Aka’ tribe who dwell in the forests of
‘I looked up and, sure enough, was the strange little creature perched upon Mohammed’s right shoulder, nervously hugging his head, and casting glances of alarm in every direction. Thus, at last, I was able to feast my eyes upon a living embodiment of the myths of some thousand years!’
Three years later two children of the Aka tribe, named Thibaut and Chair-Allah were presented to King Victor Emmanuel II in
In broad terms, a pygmy is a member of a tribe in which the top height is less than 150 centimeters (four feet and ten inches) however the shortest tribe is Efe at 135 centimeters (four feet and five inches). Furthermore, pygmies tend to have shorter legs and longer arms when compared to the average man. Also, their teeth and heads also appear to be larger that what is considered proportional.
And then there are midgets and giants.
A midget is essentially a slang term for a proportioned individual in miniature while a giant is basically a proportion, uh, giant human being. Both have been staples of the sideshow and countless human curiosity stories and both result from a similar cause.
At the base of the brain lies the pituitary gland. On average, it is the size of a pea and it secretes a total of six hormones. But the hormone is question here is growth hormone – of which it makes one thousand times more that any of the other five. Secreted into the bloodstream it tells the cells of the body to grow and divide. By entering the bloodstream, it ensures that all portions of the body grow at an equal rate.
In gigantism – the condition of being a giant, of which there are about 50 subgroups – the pituitary gland produces far too much growth hormone and is usually due to an enlarged gland. This enlargement is either genetic or the result of a tumor and mutation and in one case, that of the Irish giant Charles Byrne (pictured above), the enlarged pituitary was comparable in size to a peach.
In the case of a midget, the gland is either too small or the cells lack the receptors the growth hormone binds to. The lack of a receptor can be a mutation or genetic – as exampled by a village in the Ecuadorian Andes where and entire community, inbreed due to location, are all midgets under four feet in height.
Lastly, there is one documented case in which a man was both a dwarf and a giant during his lifetime. Adam Rainer was born in
Adam Rainer is the only person in medical history to have been classified both as a dwarf and a giant.
Portions of the article above include excepts from Mutants: On Genetic Variety and the Human Body by Armand Leroi.
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Persons with unusual skin conditions often used their affliction to their financial advantage in the world of the sideshow. The alligator-skinned (sometimes called elephant-skinned) individual became a very common attraction in the golden age of sideshow - in fact few popular sideshows were without at least one such individual. Not to be confused with the common gaff (faked display) Jake the Alligator Boy.The most severe and shocking form of congenital ichthyosis is Harlequin ichthyosis, also know as Harlequin fetus – as until recently survival of the condition was limited to mere hours after birth. Many of the children born with Harlequin ichthyosis ended up in Victorian pickled punk shows as ‘devil children’ but with the advent of modern anti-inflammatory and disinfectants some children have survived more than a decade. The affected child is born not with skin, but instead massive, diamond-shaped scales. Furthermore the eyes, ears, mouth, and other appendages can be abnormally contracted and even ‘turned inside out’. The eyelids especially can appear very disturbing. The scaly armor restricts movement to an alarming degree and because the skin is cracked where normal skin would fold, bacteria and other contaminants easily pass into the cracks and can cause lethal infections.
The term harlequin refers to the baby's facial expression and the diamond-shaped pattern of the scales. The jester and harlequins of the 17th century wore costumes with diamond patterns on them, as well as a particular style of face paint. The features of the harlequin fetus mimic this stylized makeup, and their faces are often pulled tight into grim parodies of a clown's smile.
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In regards to article I posted last week on Robley and his collection of mummified Maori heads, a reader sent me the following:
There is no precise definition of the degree of height that qualifies a person to be termed a ‘giant.’ However the term is usually applied to persons whose height is beyond the upper 1% of the average population. Typically this means that persons at or above the 7 foot mark qualify. However, in recent years the term has been used solely to describe those individuals whose height is the result of a medical condition, like pituitary gigantism, and is not commonly used to describe genetically gifted individuals.
The topic of faked marvels has been touched upon before. However, one would be foolish not to include the most famous gaff (fake) of all. The history of The Feejee Mermaid was, and continues to be, one of the most unique and enduring of all sideshow frauds.
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It is somewhat alarming to discover that many individuals born so incredibly different remain relatively unknown to history. Other than the specific nature of their afflictions, old anatomical catalogs make mention of many very special people, describe them in great detail, and yet often names – and other human aspects – are neglected or omitted. Many of these marvel of early record are baffling in their descriptions. According to Paré there was a boy born in 1493 that was ‘the result of illicit intercourse between a woman and a dog’. The creature was said to have the lower extremities of its canine father. In his 1557 book Prodigiorum ac ostentorum chronicon Conrad Lycosthenes states that in the year 1110, in the ‘Bourg of Liège’, there was born a child with the head, hands, and feet of a man, and the rest of the body like that of a pig. Lycosthenes also references the birth of a ‘serpent’ by a woman. Other animal / human hybrid marvels include a child born at Cracovia in 1547 which ‘had a head shaped like that of a man; a nose long and hooked like an elephant’s trunk; hands and feet looking like the web-foot of a goose; and a tail with a hook in it’. The child was reported to have lived for three days.
These very early accounts are likely quite true, but the descriptions attributed are simply the documenters attempt to relate what they saw in terms they and the audience could comprehend. These animal-men were most certainly human beings born with serious genetic mutations and deformities with features that in some way resembled animal characteristics. Those animal comparisons continued well into the golden age of sideshow with epithets like Lobster Boy, Dog Faced Boy, Alligator-Skinned Man, Monkey Girl and others.
Other marvels are described in legitimate detail; however, their names are lost in history. Roger of Wendover, the English chronicler, in 1062
Lycosthenes reported seeing a ‘double monster’ an infant he also states ‘took its food and drink simultaneously in its two mouths’. Another account by
Other nameless wonders include a boy born in 1529 who had two heads, four ears, four arms, but only two thighs and two legs. A rather detailed account exists of Swiss double headed man who, in 1538 at the age of thirty, ‘possessed of a beard on each face, the two bodies fused at the umbilicus into a single lower extremity. These two twins resembled one another in contour and countenance. They were so joined that at rest they looked upon one another. They had a single wife, with whom they were said to have lived in harmony’. About one hundred and fifty years later in the Gentleman's Magazine a portrait and description of a double woman was featured. Apparently the young was something of exhibition in parts of Europe but little information can be found of her and her physical situation with the exception that it was stated that she had two heads, two necks, four arms, two legs, one pelvis, and one set of pelvic organs.
These are only a few and truly it is a shame that these persons, immortalized by appearance only hundreds of year after there unique lives have ended, are anonymous. What personal stories and recollections they may have had to share. The triumphs and tribulations of the human spirit are far more interesting that the malformed bodies that vessel said spirit.
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The prodigious Julia Pastrana was known by many monikers during her life and perhaps just as many names in death. Both her life and her death are rather sad tales, but they hold a very special place in sideshow history because, for a time, she was not considered a member of the human race. Julia’s origins are shrouded in mystery. It is believed that she was born in 1834 to a tribe of ‘Root Digger’ Indians in the western slopes of
Her documented career began in 1854 as she was exhibited in
Julia then moved on to
Julia impressed many with her charm and grace. When invited to attend a military gala, she waltzed with many of the braver men there and, while in
Julia was preceded in
After
That notion was short lived and Mr. Lent, wary of loosing his investment in Julia to rivals, married her in 1857. While there is evidence that Julia was infatuated with her husband, Mr. Lent was not a kind man. While in
Julia died five days later.
During her lifetime Julia, though treated little more than an object by her promoters, did meet many influential people. She was visited by P.T. Barnum himself and even Charles Darwin acknowledged her in his book The Variation of Animal and Plants under Domestication with the words ‘Julia Pastrana, a Spanish dancer, was a remarkably fine woman – she had a thick and masculine beard’. Her condition at the time was unknown, yet given all the evidence: excessive hair, melodic voice, dental deformations and a child born with excessive hair– it is likely that she suffered from a form hypertrichosis lanuginose. All of her interviews and personal anecdotes promote the idea that she was a happy and content woman – pleased with her lot in life. Yet, one is left with a sour feeling when reflecting on the events of her life.
However, that is nothing compared to the feeling one suffers when recounting her afterlife.
Shortly after her death, Mr. Lent continued his commercial aspirations with Julia. He sold her corpse, as well as the body of his son, to Professor Sukolov of
When Mr. Lent heard of the profit his wife and child were earning in death he went about legal proceedings to reclaim them. He presented his marriage certificate to the American consul and Sukolov was forced to release the remains. Lent tried to put the mummies on display in
When the popularity of the exhibit began to fade, Lent rented the mummies to an English traveling museum of curiosities. In 1864 they were taken on a tour of
Lent and Zenora retired to
Zenora left
Gassner took the mummies to various German fairs and, in 1895, he took them to a large circus convention in
In 1943, during the German occupation, the chamber of horrors collection was ordered to be destroyed however
In 1953,
That changed in 1969 when Judge Hofheinz, a very wealthy American collector of the unusual hired a small team of detectives to track down the mummies of Julia and her child. It was a circus director named Rhodin who eventually tracked down some pamphlets and posters and made contact with Hans. Now aware of the priceless relic he now possessed, Hans instigated a bidding war only to decline all offers and put the mummies back on exhibit himself. The press picked up the story of Julia and the exhibit proved so popular that it toured
In August of 1976, the storage facility was broken into and the mummies vandalized. The child was badly damaged as its jaw and arm were torn off. His remains were thrown in a ditch outside and before it could be located – it was almost entirely eaten by mice – only scraps remained. Julia now stood alone.
In 1979, the storage facility was again broken into and this time Julia was stolen. It was presumed that it too was destroyed.
Then, in February of 1990, a Norwegian journalist discovered the mummy in the basement of the
Apparently it is still there – tucked away in some corner covered with a dusty blanket.
image: illustration byH. Konig, originally produced in the magaize Gartenlaube
Adapted from the work of Jan Bondeson and his book A Cabinet of Medical Curiosities and the book Very Special People.
ACKNOWLEDGMENTSLabels: article, bearded, hypertrichosis, women
Believe it or not, human corpulence was once an admired trait. Today, obesity is often looked at in disgust but, in the golden era of sideshow and in the 18th century – the Fat Man or Woman was a mainstay in the business of prodigious display. For some reason, persons of the time loved to see people of enormous stature – be it height or weight – and few Human Marvel exhibitions were complete without a rotund man or woman. The first person exhibited due to sheer mass is lost in history. Although, history does tend to point out some of more prolifically portly persons – though few ever were sideshow attractions. Galen, a first century Roman physician, reported meeting Nichomachus of Smyrna - a man who was so heavy that he could not move nor be moved from his bed. Other ancient texts cite the case of an unnamed Roman senator who was only able to walk when two slaves carried his belly for him, and another yarn of an Egyptian pharaoh whose belly was broader than the ‘span of a man's outstretched arms’.
Dionysius of Heracleia, who died around 305 BC, was well know in his time for his great appetite and he eventually grew so large that he could scarcely move. Furthermore, he allegedly suffered from sleep apnea and narcolepsy. His doctors feared that he would die sitting on his throne – thus servants were hired to prick him with needles should he nod off while squatting upon it. The strange treatment seemed to work as he lived to the age of fifty-five – even earning a noble reputation as large as his corpulence.
The Dutch physician Hermann Boerhaave once observed a man who took his meals at a table that ‘had been cut away in a semicircle to accommodate his circumference’. Furthermore the man ‘not having slaves to help him, used a sling worn around his shoulders to carry his belly’. In 1789 a popular Gentleman’s magazine told of a man who hadn't left his bed under his own power for three years. Allegedly pulleys were needed to accommodate a maid in changing the sheets. In 1889, an attempt was made to put a young French woman in Plaisance on exhibit. It was said that ‘eight men could not move her from her room’. As it turned out, she couldn’t fit through the door and the idea of exhibition was abandoned.
The problem with all of these tales, even those of the largest man to even walk the earth - Mills Darden - is that it is human nature to exaggerate. Even in cases where exaggeration is not evident – estimation is, thus this presented information is somewhat unreliable. So, is there any case in history where the bulk of evidence matches the human stature?
On March 13, 1770 a man was born in Leicester in
Lambert was an exceptionally bright man, possessed of a razor wit and while most came to see him out of interest and respect – he did have to deal with the occasional heckler. His retorts were legendary. On one particular occasion an obnoxious fellow was persistent and adamant in knowing the cost of Lamberts waistcoat - a rather rude question in that era – when Lambert politely refused to answer the question the heckler remarked that since he had paid a shilling (the cost of admission) toward the cost of the coat, he had a right to demand any information about it. ‘Sir,’ replied Lambert, ‘I can assure you that if I knew what part of my coat your shilling would pay for, I would cut out that piece.’
During his lifetime, Lambert was the subject of many writings including the Medical and Physical Journal, countless flyers, newspapers and caricatures and even appeared in the Memoirs of Charles Mathews (a popular actor of the era). He rubbed elbows with the affluent in influential of the time. He met King George III, visiting officers of Napoleon, royalty, ambassadors and even an elderly Josef Boruwlaski – certainly a stunning meeting as the biggest man of that time met the smallest.
When Lambert died in 1808, still in relative good health except for nagging knees, he weighed in at 739 pounds. His waist measured 9 feet and 4 inches. He was immensely popular due to his wit and easy going nature. People were in awe of not only his size, but of his spirit as well. Many regarded him as a true jovial, gentle giant - a reputation that would carry to the big jolly sideshow men and women who would follow in his ample shoes for decades.
Following his death, Lambert was featured in his own biography: The Life of that Wonderful and Extraordinary Heavy Man, the late Daniel Lambert. He was also featured in Granger’s Wonderful Museum and Magazine Extraordinary, Smeeton’s Biographia Curiosa. He is referred to in great novels like Barry Lyndon, Vanity Fair and even Charles Dickenson’s Nicholas Nickleby. Lambert’s popularity even spread to
It was also Dickens who, in his magazine Household Words forever cemented the name Daniel Lambert with hugeness. Even today, there are numerous Pubs, Taverns and Inns named after Lambert – with the keepers hoping the clientele will associate the name with ample portions of food and drink. Oddly enough, Lambert likely suffered from a pituitary obesity – he reputedly never ate a large meal or drank beer.
The Mountainous Human Marvel is all but gone now, with only one Fat Man, Howard Huge, still traveling. The obese are no longer looked upon in wonder, interest and awe - rather with disgust and insensitivity. In fact just a few short years ago, at St. Martin's churchyard in
Adapted from the book The Two Headed Boy by Jan Bondeson .
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The sixteenth- and seventeenth-century must have been a simply enchanting time as fairy-tales seemed to spring into reality and the shelves of cabinets of curiosities overflowed with unusual items. The old stories of wee folk, giants and misshapen monsters seemed to be confirmed reality and in 1556 it seemed as though werewolves were also a factual entity when Petrus Gonzales stepped forward into the light of history.